Dermatofibrosarcoma protuberans (DFSP) is a rare cutaneous tumour, representing approximately 0.1% of cutaneous malignancies. They can be locally invasive and have a recurrence rate of up to 60%, but have low metastatic potential. We present a case of a 30-year-old female in Far North Queensland with a DFSP arising in a chronic keloid scar on her upper chest. The lesion was widely excised to pectoralis major muscle and reconstructed with a free parascapular flap. We also reviewed the available literature on this phenomenon, finding only two other reported cases of DFSP arising in keloid scar.